What is the long Q-T syndrome LQTS? Long Q-T syndrome is an infrequent, hereditary disorder of the heart"s electrical rhythm that can occur in otherwise-healthy people. It usually affects children or young adults. When the heart contracts, it emits an electrical signal. This signal can be recorded on an electrocardiogram ECG or EKG and produces a characteristic waveform. The different parts of this waveform are designated by letters -- P, Q, R, S and T. The Q-T interval represents the time for electrical activation and inactivation of the ventricles, the heart"s lower chambers. A doctor can measure the time it...
Thus, when they have an ECG as during a routine physical examination, the Q-T interval may be normal.

Some healthy young people may not have a routine ECG, and LQTS may be suspected because of their family history or because of unexplained fainting episodes. In any family where repeated episodes of fainting or a history of sudden death exist, the causes, including long Q-T syndrome, should be investigated.

How is LQTS treated?

There are treatments for long Q-T syndrome, including medications such as beta blockers. Sometimes a surgical procedure is needed. Some people may benefit from an implantable defibrillator.